%0 Journal Article %A Janssens, Geert O %A Gandola, Lorenza %A Bolle, Stephanie %A Mandeville, Henry %A Ramos-Albiac, Monica %A van Beek, Karen %A Benghiat, Helen %A Hoeben, Bianca %A Morales La Madrid, Andres %A Kortmann, Rolf-Dieter %A Hargrave, Darren %A Menten, Johan %A Pecori, Emilia %A Biassoni, Veronica %A von Bueren, Andre O %A van Vuurden, Dannis G %A Massimino, Maura %A Sturm, Dominik %A Peters, Max %A Kramm, Christof M %T Survival benefit for patients with diffuse intrinsic pontine glioma (DIPG) undergoing re-irradiation at first progression: A matched-cohort analysis on behalf of the SIOP-E-HGG/DIPG working group. %J European journal of cancer %V 73 %@ 0959-8049 %C Amsterdam [u.a.] %I Elsevier %M DKFZ-2017-00925 %P 38 - 47 %D 2017 %X Overall survival (OS) of patients with diffuse intrinsic pontine glioma (DIPG) is poor. The purpose of this study is to analyse benefit and toxicity of re-irradiation at first progression.At first progression, 31 children with DIPG, aged 2-16 years, underwent re-irradiation (dose 19.8-30.0 Gy) alone (n = 16) or combined with systemic therapy (n = 15). At initial presentation, all patients had typical symptoms and characteristic MRI features of DIPG, or biopsy-proven high-grade glioma. An interval of ≥3 months after upfront radiotherapy was required before re-irradiation. Thirty-nine patients fulfilling the same criteria receiving radiotherapy at diagnosis, followed by best supportive care (n = 20) or systemic therapy (n = 19) at progression but no re-irradiation, were eligible for a matched-cohort analysis.Median OS for patients undergoing re-irradiation was 13.7 months. For a similar median progression-free survival after upfront radiotherapy (8.2 versus 7.7 months; P = .58), a significant benefit in median OS (13.7 versus 10.3 months; P = .04) was observed in favour of patients undergoing re-irradiation. Survival benefit of re-irradiation increased with a longer interval between end-of-radiotherapy and first progression (3-6 months: 4.0 versus 2.7; P < .01; 6-12 months: 6.4 versus 3.3; P = .04). Clinical improvement with re-irradiation was observed in 24/31 (77 %F PUB:(DE-HGF)16 %9 Journal Article %$ pmid:28161497 %R 10.1016/j.ejca.2016.12.007 %U https://inrepo02.dkfz.de/record/120496