000124245 001__ 124245 000124245 005__ 20240228145501.0 000124245 0247_ $$2doi$$a10.1093/neuonc/now234 000124245 0247_ $$2pmid$$apmid:28011926 000124245 0247_ $$2pmc$$apmc:PMC5464312 000124245 0247_ $$2ISSN$$a1522-8517 000124245 0247_ $$2ISSN$$a1523-5866 000124245 0247_ $$2altmetric$$aaltmetric:30752855 000124245 037__ $$aDKFZ-2017-01141 000124245 041__ $$aeng 000124245 082__ $$a610 000124245 1001_ $$aMynarek, Martin$$b0 000124245 245__ $$aEvaluation of age-dependent treatment strategies for children and young adults with pineoblastoma: analysis of pooled European Society for Paediatric Oncology (SIOP-E) and US Head Start data. 000124245 260__ $$aOxford$$bOxford Univ. Press$$c2017 000124245 3367_ $$2DRIVER$$aarticle 000124245 3367_ $$2DataCite$$aOutput Types/Journal article 000124245 3367_ $$0PUB:(DE-HGF)16$$2PUB:(DE-HGF)$$aJournal Article$$bjournal$$mjournal$$s1510823592_26038 000124245 3367_ $$2BibTeX$$aARTICLE 000124245 3367_ $$2ORCID$$aJOURNAL_ARTICLE 000124245 3367_ $$00$$2EndNote$$aJournal Article 000124245 520__ $$aPineoblastoma is a rare pineal region brain tumor. Treatment strategies have reflected those for other malignant embryonal brain tumors.Original prospective treatment and outcome data from international trial groups were pooled. Cox regression models were developed considering treatment elements as time-dependent covariates.Data on 135 patients with pineoblastoma aged 0.01-20.7 (median 4.9) years were analyzed. Median observation time was 7.3 years. Favorable prognostic factors were age ≥4 years (hazard ratio [HR] for progression-free survival [PFS] 0.270, P < .001) and administration of radiotherapy (HR for PFS 0.282, P < .001). Metastatic disease (HR for PFS 2.015, P = .006), but not postoperative residual tumor, was associated with unfavorable prognosis. In 57 patients <4 years old, 5-year PFS/overall survival (OS) were 11 ± 4%/12 ± 4%. Two patients survived after chemotherapy only, while 3 of 16 treated with craniospinal irradiation (CSI) with boost, and 3 of 5 treated with high-dose chemotherapy (HDCT) and local radiotherapy survived. In 78 patients aged ≥4 years, PFS/OS were 72 ± 7%/73 ± 7% for patients without metastases, and 50 ± 10%/55 ± 10% with metastases. Seventy-three patients received radiotherapy (48 conventionally fractionated CSI, median dose 35.0 [18.0-45.0] Gy, 19 hyperfractionated CSI, 6 local radiotherapy), with (n = 68) or without (n = 6) chemotherapy. The treatment sequence had no impact; application of HDCT had weak impact on survival in older patients.Survival is poor in young children treated without radiotherapy. In these patients, combination of HDCT and local radiotherapy may warrant further evaluation in the absence of more specific or targeted treatments. CSI combined with chemotherapy is effective for older non-metastatic patients. 000124245 536__ $$0G:(DE-HGF)POF3-312$$a312 - Functional and structural genomics (POF3-312)$$cPOF3-312$$fPOF III$$x0 000124245 588__ $$aDataset connected to CrossRef, PubMed, 000124245 7001_ $$aPizer, Barry$$b1 000124245 7001_ $$aDufour, Christelle$$b2 000124245 7001_ $$avan Vuurden, Dannis$$b3 000124245 7001_ $$aGarami, Miklos$$b4 000124245 7001_ $$aMassimino, Maura$$b5 000124245 7001_ $$aFangusaro, Jason$$b6 000124245 7001_ $$aDavidson, Tom$$b7 000124245 7001_ $$aGil-da-Costa, Maria Joao$$b8 000124245 7001_ $$aSterba, Jaroslav$$b9 000124245 7001_ $$aBenesch, Martin$$b10 000124245 7001_ $$aGerber, Nicolas$$b11 000124245 7001_ $$aJuhnke, B Ole$$b12 000124245 7001_ $$aKwiecien, Robert$$b13 000124245 7001_ $$aPietsch, Torsten$$b14 000124245 7001_ $$0P:(DE-He78)4c28e2aade5f44d8eca9dd8e97638ec8$$aKool, Marcel$$b15$$udkfz 000124245 7001_ $$aClifford, Steve$$b16 000124245 7001_ $$aEllison, David W$$b17 000124245 7001_ $$aGiangaspero, Felice$$b18 000124245 7001_ $$aWesseling, Pieter$$b19 000124245 7001_ $$aGilles, Floyd$$b20 000124245 7001_ $$aGottardo, Nicholas$$b21 000124245 7001_ $$aFinlay, Jonathan L$$b22 000124245 7001_ $$aRutkowski, Stefan$$b23 000124245 7001_ $$avon Hoff, Katja$$b24 000124245 773__ $$0PERI:(DE-600)2094060-9$$a10.1093/neuonc/now234$$gVol. 19, no. 4, p. now234 -$$n4$$p576-585$$tNeuro-Oncology$$v19$$x1523-5866$$y2017 000124245 909CO $$ooai:inrepo02.dkfz.de:124245$$pVDB 000124245 9101_ $$0I:(DE-588b)2036810-0$$6P:(DE-He78)4c28e2aade5f44d8eca9dd8e97638ec8$$aDeutsches Krebsforschungszentrum$$b15$$kDKFZ 000124245 9131_ $$0G:(DE-HGF)POF3-312$$1G:(DE-HGF)POF3-310$$2G:(DE-HGF)POF3-300$$3G:(DE-HGF)POF3$$4G:(DE-HGF)POF$$aDE-HGF$$bGesundheit$$lKrebsforschung$$vFunctional and structural genomics$$x0 000124245 9141_ $$y2017 000124245 915__ $$0StatID:(DE-HGF)0400$$2StatID$$aAllianz-Lizenz / DFG 000124245 915__ $$0StatID:(DE-HGF)0420$$2StatID$$aNationallizenz 000124245 915__ $$0StatID:(DE-HGF)0100$$2StatID$$aJCR$$bNEURO-ONCOLOGY : 2015 000124245 915__ $$0StatID:(DE-HGF)0200$$2StatID$$aDBCoverage$$bSCOPUS 000124245 915__ $$0StatID:(DE-HGF)0300$$2StatID$$aDBCoverage$$bMedline 000124245 915__ $$0StatID:(DE-HGF)0310$$2StatID$$aDBCoverage$$bNCBI Molecular Biology Database 000124245 915__ $$0StatID:(DE-HGF)0199$$2StatID$$aDBCoverage$$bThomson Reuters Master Journal List 000124245 915__ $$0StatID:(DE-HGF)0111$$2StatID$$aWoS$$bScience Citation Index Expanded 000124245 915__ $$0StatID:(DE-HGF)0150$$2StatID$$aDBCoverage$$bWeb of Science Core Collection 000124245 915__ $$0StatID:(DE-HGF)1110$$2StatID$$aDBCoverage$$bCurrent Contents - Clinical Medicine 000124245 915__ $$0StatID:(DE-HGF)9905$$2StatID$$aIF >= 5$$bNEURO-ONCOLOGY : 2015 000124245 9201_ $$0I:(DE-He78)B062-20160331$$kB062$$lPädiatrische Neuroonkologie$$x0 000124245 980__ $$ajournal 000124245 980__ $$aVDB 000124245 980__ $$aI:(DE-He78)B062-20160331 000124245 980__ $$aUNRESTRICTED