TY - JOUR AU - Mynarek, Martin AU - Pizer, Barry AU - Dufour, Christelle AU - van Vuurden, Dannis AU - Garami, Miklos AU - Massimino, Maura AU - Fangusaro, Jason AU - Davidson, Tom AU - Gil-da-Costa, Maria Joao AU - Sterba, Jaroslav AU - Benesch, Martin AU - Gerber, Nicolas AU - Juhnke, B Ole AU - Kwiecien, Robert AU - Pietsch, Torsten AU - Kool, Marcel AU - Clifford, Steve AU - Ellison, David W AU - Giangaspero, Felice AU - Wesseling, Pieter AU - Gilles, Floyd AU - Gottardo, Nicholas AU - Finlay, Jonathan L AU - Rutkowski, Stefan AU - von Hoff, Katja TI - Evaluation of age-dependent treatment strategies for children and young adults with pineoblastoma: analysis of pooled European Society for Paediatric Oncology (SIOP-E) and US Head Start data. JO - Neuro-Oncology VL - 19 IS - 4 SN - 1523-5866 CY - Oxford PB - Oxford Univ. Press M1 - DKFZ-2017-01141 SP - 576-585 PY - 2017 AB - Pineoblastoma is a rare pineal region brain tumor. Treatment strategies have reflected those for other malignant embryonal brain tumors.Original prospective treatment and outcome data from international trial groups were pooled. Cox regression models were developed considering treatment elements as time-dependent covariates.Data on 135 patients with pineoblastoma aged 0.01-20.7 (median 4.9) years were analyzed. Median observation time was 7.3 years. Favorable prognostic factors were age ≥4 years (hazard ratio [HR] for progression-free survival [PFS] 0.270, P < .001) and administration of radiotherapy (HR for PFS 0.282, P < .001). Metastatic disease (HR for PFS 2.015, P = .006), but not postoperative residual tumor, was associated with unfavorable prognosis. In 57 patients <4 years old, 5-year PFS/overall survival (OS) were 11 ± 4 LB - PUB:(DE-HGF)16 C6 - pmid:28011926 C2 - pmc:PMC5464312 DO - DOI:10.1093/neuonc/now234 UR - https://inrepo02.dkfz.de/record/124245 ER -