000126905 001__ 126905 000126905 005__ 20240228140853.0 000126905 0247_ $$2doi$$a10.1111/neup.12227 000126905 0247_ $$2pmid$$apmid:26183384 000126905 0247_ $$2ISSN$$a0919-6544 000126905 0247_ $$2ISSN$$a1440-1789 000126905 0247_ $$2altmetric$$aaltmetric:4284181 000126905 037__ $$aDKFZ-2017-02933 000126905 041__ $$aeng 000126905 082__ $$a610 000126905 1001_ $$0P:(DE-He78)8d9c904a6cea14d4c99c78ba46e41f93$$aKorshunov, Andrey$$b0$$eFirst author$$udkfz 000126905 245__ $$aComparative integrated molecular analysis of intraocular medulloepitheliomas and central nervous system embryonal tumors with multilayered rosettes confirms that they are distinct nosologic entities. 000126905 260__ $$aOxford [u.a.]$$bWiley-Blackwell$$c2015 000126905 3367_ $$2DRIVER$$aarticle 000126905 3367_ $$2DataCite$$aOutput Types/Journal article 000126905 3367_ $$0PUB:(DE-HGF)16$$2PUB:(DE-HGF)$$aJournal Article$$bjournal$$mjournal$$s1508498929_28027 000126905 3367_ $$2BibTeX$$aARTICLE 000126905 3367_ $$2ORCID$$aJOURNAL_ARTICLE 000126905 3367_ $$00$$2EndNote$$aJournal Article 000126905 520__ $$aIntraocular medulloepithelioma (IO MEPL) is an uncommon embryonal neuroepithelial neoplasm of the eye. These ocular neoplasms have been compared with intracranial medulloepitheliomas or other histologic variants of CNS embryonal tumor with multilayered rosettes (CNS ETMR) due to their morphological mimicry. We performed comprehensive molecular analysis to explore the histogenetic and biologic relationships between 22 IO MEPL and 68 CNS ETMR. Routinely prepared paraffin-embedded samples were assessed for genome-wide methylation profiles using the Illumina Methylation 450k BeadChip array. We identified strong cytogenetic and epigenetic differences between ocular neoplasms and CNS ETMR. None of the IO MEPL cases displayed the ETMR-specific amplification of the C19MC locus. Instead, cytogenetic analysis of the IO MEPL showed numerous copy number aberrations which involved either whole chromosomes or chromosomal arms; recurrent aberrations in these tumors affected chromosomes 1p, 4, 8 and 16p. DNA methylation patterns were also strikingly different between these two tumor entities, suggesting that they do not share common origins and biological behaviors. Comparative cluster analysis of 198 pediatric CNS tumors and 22 IO MEPL revealed a clear demarcation of the CNS ETMR and IO MEPL profiles from other CNS entities. In conclusion, although IO MEPL shares some histopathological features with CNS ETMR, they manifest striking molecular diversity at the cytogenetic and epigenetic levels. Consequently they deserve a separate nosologic designation in future tumor classifications, where CNS MEPL could be designated as a histological variant of CNS ETMR. 000126905 536__ $$0G:(DE-HGF)POF3-312$$a312 - Functional and structural genomics (POF3-312)$$cPOF3-312$$fPOF III$$x0 000126905 588__ $$aDataset connected to CrossRef, PubMed, 000126905 7001_ $$aJakobiec, Frederick A$$b1 000126905 7001_ $$aEberhart, Charles G$$b2 000126905 7001_ $$0P:(DE-He78)744146d3b5a3df1e0ac555e5bf1ee5cc$$aHovestadt, Volker$$b3$$udkfz 000126905 7001_ $$0P:(DE-He78)51bf9ae9cb5771b30c483e5597ef606c$$aCapper, David$$b4$$udkfz 000126905 7001_ $$0P:(DE-He78)551bb92841f634070997aa168d818492$$aJones, David$$b5$$udkfz 000126905 7001_ $$0P:(DE-He78)a46a5b2a871859c8e2d63d2f8c666807$$aSturm, Dominik$$b6$$udkfz 000126905 7001_ $$aStagner, Anna M$$b7 000126905 7001_ $$aEdward, Deepak P$$b8 000126905 7001_ $$aEagle, Ralph C$$b9 000126905 7001_ $$aProia, Alan D$$b10 000126905 7001_ $$aKoch, Arend$$b11 000126905 7001_ $$aRyzhova, Marina$$b12 000126905 7001_ $$aEktova, Anastasia$$b13 000126905 7001_ $$aSchüller, Ulrich$$b14 000126905 7001_ $$aZheludkova, Olga$$b15 000126905 7001_ $$0P:(DE-He78)e13b4363c5fe858044ef8a39c02c870c$$aLichter, Peter$$b16$$udkfz 000126905 7001_ $$0P:(DE-He78)a8a10626a848d31e70cfd96a133cc144$$avon Deimling, Andreas$$b17$$udkfz 000126905 7001_ $$0P:(DE-He78)f746aa965c4e1af518b016de3aaff5d9$$aPfister, Stefan$$b18$$udkfz 000126905 7001_ $$0P:(DE-He78)4c28e2aade5f44d8eca9dd8e97638ec8$$aKool, Marcel$$b19$$eLast author$$udkfz 000126905 773__ $$0PERI:(DE-600)2008290-3$$a10.1111/neup.12227$$gVol. 35, no. 6, p. 538 - 544$$n6$$p538 - 544$$tNeuropathology$$v35$$x0919-6544$$y2015 000126905 909CO $$ooai:inrepo02.dkfz.de:126905$$pVDB 000126905 9101_ $$0I:(DE-588b)2036810-0$$6P:(DE-He78)8d9c904a6cea14d4c99c78ba46e41f93$$aDeutsches Krebsforschungszentrum$$b0$$kDKFZ 000126905 9101_ $$0I:(DE-588b)2036810-0$$6P:(DE-He78)744146d3b5a3df1e0ac555e5bf1ee5cc$$aDeutsches Krebsforschungszentrum$$b3$$kDKFZ 000126905 9101_ $$0I:(DE-588b)2036810-0$$6P:(DE-He78)51bf9ae9cb5771b30c483e5597ef606c$$aDeutsches Krebsforschungszentrum$$b4$$kDKFZ 000126905 9101_ $$0I:(DE-588b)2036810-0$$6P:(DE-He78)551bb92841f634070997aa168d818492$$aDeutsches Krebsforschungszentrum$$b5$$kDKFZ 000126905 9101_ $$0I:(DE-588b)2036810-0$$6P:(DE-He78)a46a5b2a871859c8e2d63d2f8c666807$$aDeutsches Krebsforschungszentrum$$b6$$kDKFZ 000126905 9101_ $$0I:(DE-588b)2036810-0$$6P:(DE-He78)e13b4363c5fe858044ef8a39c02c870c$$aDeutsches Krebsforschungszentrum$$b16$$kDKFZ 000126905 9101_ $$0I:(DE-588b)2036810-0$$6P:(DE-He78)a8a10626a848d31e70cfd96a133cc144$$aDeutsches Krebsforschungszentrum$$b17$$kDKFZ 000126905 9101_ $$0I:(DE-588b)2036810-0$$6P:(DE-He78)f746aa965c4e1af518b016de3aaff5d9$$aDeutsches Krebsforschungszentrum$$b18$$kDKFZ 000126905 9101_ $$0I:(DE-588b)2036810-0$$6P:(DE-He78)4c28e2aade5f44d8eca9dd8e97638ec8$$aDeutsches Krebsforschungszentrum$$b19$$kDKFZ 000126905 9131_ $$0G:(DE-HGF)POF3-312$$1G:(DE-HGF)POF3-310$$2G:(DE-HGF)POF3-300$$3G:(DE-HGF)POF3$$4G:(DE-HGF)POF$$aDE-HGF$$bGesundheit$$lKrebsforschung$$vFunctional and structural genomics$$x0 000126905 9141_ $$y2015 000126905 915__ $$0StatID:(DE-HGF)0200$$2StatID$$aDBCoverage$$bSCOPUS 000126905 915__ $$0StatID:(DE-HGF)0300$$2StatID$$aDBCoverage$$bMedline 000126905 915__ $$0StatID:(DE-HGF)0310$$2StatID$$aDBCoverage$$bNCBI Molecular Biology Database 000126905 915__ $$0StatID:(DE-HGF)0100$$2StatID$$aJCR$$bNEUROPATHOLOGY : 2015 000126905 915__ $$0StatID:(DE-HGF)0600$$2StatID$$aDBCoverage$$bEbsco Academic Search 000126905 915__ $$0StatID:(DE-HGF)0030$$2StatID$$aPeer Review$$bASC 000126905 915__ $$0StatID:(DE-HGF)0199$$2StatID$$aDBCoverage$$bThomson Reuters Master Journal List 000126905 915__ $$0StatID:(DE-HGF)0111$$2StatID$$aWoS$$bScience Citation Index Expanded 000126905 915__ $$0StatID:(DE-HGF)0150$$2StatID$$aDBCoverage$$bWeb of Science Core Collection 000126905 915__ $$0StatID:(DE-HGF)9900$$2StatID$$aIF < 5 000126905 9201_ $$0I:(DE-He78)G380-20160331$$kG380$$lKKE Neuropathologie$$x0 000126905 9201_ $$0I:(DE-He78)B060-20160331$$kB060$$lMolekulare Genetik$$x1 000126905 9201_ $$0I:(DE-He78)B062-20160331$$kB062$$lPädiatrische Neuroonkologie$$x2 000126905 9201_ $$0I:(DE-He78)L101-20160331$$kL101$$lDKTK Heidelberg$$x3 000126905 9201_ $$0I:(DE-He78)L701-20160331$$kL701$$lDKTK München$$x4 000126905 980__ $$ajournal 000126905 980__ $$aVDB 000126905 980__ $$aI:(DE-He78)G380-20160331 000126905 980__ $$aI:(DE-He78)B060-20160331 000126905 980__ $$aI:(DE-He78)B062-20160331 000126905 980__ $$aI:(DE-He78)L101-20160331 000126905 980__ $$aI:(DE-He78)L701-20160331 000126905 980__ $$aUNRESTRICTED