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@ARTICLE{Oh:130276,
author = {S. Oh and R. A. Flynn and S. N. Floor and J. Purzner and L.
Martin and B. T. Do and S. Schubert and D. Vaka and S.
Morrissy and Y. Li and M. Kool$^*$ and V. Hovestadt$^*$ and
D. Jones$^*$ and P. A. Northcott$^*$ and T. Risch and H.-J.
Warnatz and M.-L. Yaspo and C. M. Adams and R. D. Leib and
M. Breese and M. A. Marra and D. Malkin and P. Lichter$^*$
and J. A. Doudna and S. Pfister$^*$ and M. D. Taylor and H.
Y. Chang and Y.-J. Cho},
title = {{M}edulloblastoma-associated {DDX}3 variant selectively
alters the translational response to stress.},
journal = {OncoTarget},
volume = {7},
number = {19},
issn = {1949-2553},
address = {[S.l.]},
publisher = {Impact Journals LLC},
reportid = {DKFZ-2017-05355},
pages = {28169 - 28182},
year = {2016},
abstract = {DDX3X encodes a DEAD-box family RNA helicase (DDX3)
commonly mutated in medulloblastoma, a highly aggressive
cerebellar tumor affecting both children and adults. Despite
being implicated in several facets of RNA metabolism, the
nature and scope of DDX3s interactions with RNA remain
unclear. Here, we show DDX3 collaborates extensively with
the translation initiation machinery through direct binding
to 5UTRs of nearly all coding RNAs, specific sites on the
18S rRNA, and multiple components of the translation
initiation complex. Impairment of translation initiation is
also evident in primary medulloblastomas harboring mutations
in DDX3X, further highlighting DDX3s role in this process.
Arsenite-induced stress shifts DDX3 binding from the 5UTR
into the coding region of mRNAs concomitant with a general
reduction of translation, and both the shift of DDX3 on mRNA
and decreased translation are blunted by expression of a
catalytically-impaired, medulloblastoma-associated DDX3R534H
variant. Furthermore, despite the global repression of
translation induced by arsenite, translation is preserved on
select genes involved in chromatin organization in
DDX3R534H-expressing cells. Thus, DDX3 interacts extensively
with RNA and ribosomal machinery to help remodel the
translation landscape in response to stress, while
cancer-related DDX3 variants adapt this response to
selectively preserve translation.},
cin = {B062 / B060},
ddc = {610},
cid = {I:(DE-He78)B062-20160331 / I:(DE-He78)B060-20160331},
pnm = {312 - Functional and structural genomics (POF3-312)},
pid = {G:(DE-HGF)POF3-312},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:27058758},
pmc = {pmc:PMC5053718},
doi = {10.18632/oncotarget.8612},
url = {https://inrepo02.dkfz.de/record/130276},
}