% IMPORTANT: The following is UTF-8 encoded. This means that in the presence % of non-ASCII characters, it will not work with BibTeX 0.99 or older. % Instead, you should use an up-to-date BibTeX implementation like “bibtex8” or % “biber”. @ARTICLE{Weber:130829, author = {M.-A. Weber$^*$ and A. Nagel$^*$ and A. Marschar$^*$ and P. A. Glemser$^*$ and K. Jurkat-Rott and M. B. Wolf$^*$ and M. Ladd$^*$ and H.-P. Schlemmer$^*$ and H.-U. Kauczor and F. Lehmann-Horn}, title = {7-{T} (35){C}l and (23){N}a {MR} {I}maging for {D}etection of {M}utation-dependent {A}lterations in {M}uscular {E}dema and {F}at {F}raction with {S}odium and {C}hloride {C}oncentrations in {M}uscular {P}eriodic {P}aralyses.}, journal = {Radiology}, volume = {280}, number = {3}, issn = {1527-1315}, address = {Oak Brook, Ill.}, publisher = {Soc.}, reportid = {DKFZ-2017-05907}, pages = {848 - 859}, year = {2016}, abstract = {Purpose To determine whether altered sodium (Na(+)) and chloride (Cl(-)) homeostasis can be visualized in periodic paralyses by using 7-T sodium 23 ((23)Na) and chlorine 35 ((35)Cl) magnetic resonance (MR) imaging. Materials and Methods Institutional review board approval and informed consent of all participants were obtained. (23)Na (repetition time msec/echo time msec, 160/0.35) and (35)Cl (40/0.6) MR imaging of both lower legs was performed with a 7-T whole-body system in patients with genetically confirmed hypokalemic periodic paralysis (Cav1.1-R1239H mutation, n = 5; Cav1.1-R528H mutation, n = 8) and Andersen-Tawil syndrome (n = 3) and in 16 healthy volunteers. Additionally, each participant underwent 3-T proton MR imaging on the same day by using T1-weighted, short-tau inversion-recovery, and Dixon-type sequences. Muscle edema was assessed on short-tau inversion-recovery images, fatty degeneration was assessed on T1-weighted images, and muscular fat fraction was quantified with Dixon-type imaging. Na(+) and Cl(-) were quantified in the soleus muscle by using three phantoms that contained 10-, 20-, and 30-mmol/L NaCl solution and $5\%$ agarose gel as a reference. Parametric data for all subpopulations were tested by using one-way analysis of variance with the Dunnett test, and correlations were assessed with the Spearman rank correlation coefficient. Results Median muscular (23)Na concentration was higher in patients with Cav1.1-R1239H (34.7 mmol/L, P < .001), Cav1.1-R528H (32.0 mmol/L, P < .001), and Kir2.1 (24.3 mmol/L, P = .035) mutations than in healthy volunteers (19.9 mmol/L). Median muscular normalized (35)Cl signal intensity was higher in patients with Cav1.1-R1239H (27.6, P < .001) and Cav1.1-R528H (23.6, P < .001) than in healthy volunteers (12.6), but not in patients with the Kir2.1 mutation (14.3, P = .517). When compared with volunteers, patients with Cav1.1-R1239H and Cav1.1-R528H showed increased muscular edema (P < .001 and P = .003, respectively) and muscle fat fraction (P < .001 and P = .017, respectively). Conclusion With 7-T MR imaging, changes of Na(+) and Cl(-) homeostasis can be visualized in periodic paralyses and are most pronounced in the severe phenotype Cav1.1-R1239H, with up to daily paralytic episodes. (©) RSNA, 2016 An earlier incorrect version of this article appeared online. This article was corrected on April 18, 2016.}, keywords = {Sodium Isotopes (NLM Chemicals) / Chlorine (NLM Chemicals)}, cin = {E010 / E020 / E015}, ddc = {610}, cid = {I:(DE-He78)E010-20160331 / I:(DE-He78)E020-20160331 / I:(DE-He78)E015-20160331}, pnm = {315 - Imaging and radiooncology (POF3-315)}, pid = {G:(DE-HGF)POF3-315}, typ = {PUB:(DE-HGF)16}, pubmed = {pmid:27082780}, doi = {10.1148/radiol.2016151617}, url = {https://inrepo02.dkfz.de/record/130829}, }