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@ARTICLE{Rud:132855,
author = {R. Rudà and G. Reifenberger$^*$ and D. Frappaz and S.
Pfister$^*$ and A. Laprie and T. Santarius and P. Roth and
J. C. Tonn$^*$ and R. Soffietti and M. Weller and E. C.
Moyal},
title = {{EANO} guidelines for the diagnosis and treatment of
ependymal tumors.},
journal = {Neuro-Oncology},
volume = {20},
number = {4},
issn = {1523-5866},
address = {Oxford},
publisher = {Oxford Univ. Press},
reportid = {DKFZ-2018-00498},
pages = {445 - 456},
year = {2018},
abstract = {Ependymal tumors are rare CNS tumors and may occur at any
age, but their proportion among primary brain tumors is
highest in children and young adults. Thus, the level of
evidence of diagnostic and therapeutic interventions is
higher in the pediatric compared with the adult patient
population.The diagnosis and disease staging is performed by
craniospinal MRI. Tumor classification is achieved by
histological and molecular diagnostic assessment of tissue
specimens according to the World Health Organization (WHO)
classification 2016. Surgery is the crucial initial
treatment in both children and adults. In pediatric patients
with intracranial ependymomas of WHO grades II or III,
surgery is followed by local radiotherapy regardless of
residual tumor volume. In adults, radiotherapy is employed
in patients with anaplastic ependymoma WHO grade III, and in
case of incomplete resection of WHO grade II ependymoma.
Chemotherapy alone is reserved for young children <12 months
and for adults with recurrent disease when further surgery
and irradiation are no longer feasible. A gross total
resection is the mainstay of treatment in spinal
ependymomas, and radiotherapy is reserved for incompletely
resected tumors. Nine subgroups of ependymal tumors across
different anatomical compartments (supratentorial, posterior
fossa, spinal) and patient ages have been identified with
distinct genetic and epigenetic alterations, and with
distinct outcomes. These findings may lead to more precise
diagnostic and prognostic assessments, molecular
subgroup-adapted therapies, and eventually new
recommendations pending validation in prospective studies.},
subtyp = {Review Article},
cin = {L401 / B062 / L101 / L701},
ddc = {610},
cid = {I:(DE-He78)L401-20160331 / I:(DE-He78)B062-20160331 /
I:(DE-He78)L101-20160331 / I:(DE-He78)L701-20160331},
pnm = {312 - Functional and structural genomics (POF3-312)},
pid = {G:(DE-HGF)POF3-312},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:29194500},
pmc = {pmc:PMC5909649},
doi = {10.1093/neuonc/nox166},
url = {https://inrepo02.dkfz.de/record/132855},
}