% IMPORTANT: The following is UTF-8 encoded. This means that in the presence
% of non-ASCII characters, it will not work with BibTeX 0.99 or older.
% Instead, you should use an up-to-date BibTeX implementation like “bibtex8” or
% “biber”.
@ARTICLE{Reinhardt:147394,
author = {A. Reinhardt$^*$ and D. Stichel$^*$ and D. Schrimpf$^*$ and
C. Koelsche$^*$ and A. K. Wefers$^*$ and A. Ebrahimi$^*$ and
P. Sievers$^*$ and K. Huang$^*$ and M. B. Casalini$^*$ and
F. Fernández-Klett$^*$ and A. Suwala$^*$ and M. Weller and
D. Gramatzki and J. Felsberg and G. Reifenberger$^*$ and A.
Becker and V. H. Hans and M. Prinz and O. Staszewski and T.
Acker and H. Dohmen and C. Hartmann and W. Paulus and K.
Heß and B. Brokinkel and J. Schittenhelm and R. Buslei and
M. Deckert and C. Mawrin and E. Hewer and U. Pohl and Z.
Jaunmuktane and S. Brandner and A. Unterberg and D. Hänggi
and M. Platten$^*$ and S. M. Pfister$^*$ and W. Wick and C.
Herold-Mende and A. Korshunov$^*$ and D. E. Reuss$^*$ and F.
Sahm$^*$ and D. T. W. Jones$^*$ and D. Capper$^*$ and A. von
Deimling$^*$},
title = {{T}umors diagnosed as cerebellar glioblastoma comprise
distinct molecular entities.},
journal = {Acta Neuropathologica Communications},
volume = {7},
number = {1},
issn = {2051-5960},
address = {London},
publisher = {Biomed Central},
reportid = {DKFZ-2019-02511},
pages = {163},
year = {2019},
note = {EA:B300LA:B300},
abstract = {In this multi-institutional study we compiled a
retrospective cohort of 86 posterior fossa tumors having
received the diagnosis of cerebellar glioblastoma (cGBM).
All tumors were reviewed histologically and subjected to
array-based methylation analysis followed by algorithm-based
classification into distinct methylation classes (MCs). The
single MC containing the largest proportion of 25 tumors
diagnosed as cGBM was MC anaplastic astrocytoma with piloid
features representing a recently-described molecular tumor
entity not yet included in the WHO Classification of Tumours
of the Central Nervous System (WHO classification).
Twenty-nine tumors molecularly corresponded to either of 6
methylation subclasses subsumed in the MC family GBM IDH
wildtype. Further we identified 6 tumors belonging to the MC
diffuse midline glioma H3 K27 M mutant and 6 tumors
allotted to the MC IDH mutant glioma subclass astrocytoma.
Two tumors were classified as MC pilocytic astrocytoma of
the posterior fossa, one as MC CNS high grade
neuroepithelial tumor with BCOR alteration and one as MC
control tissue, inflammatory tumor microenvironment. The
methylation profiles of 16 tumors could not clearly be
assigned to one distinct MC. In comparison to supratentorial
localization, the MC GBM IDH wildtype subclass midline was
overrepresented, whereas the MCs GBM IDH wildtype subclass
mesenchymal and subclass RTK II were underrepresented in the
cerebellum. Based on the integration of molecular and
histological findings all tumors received an integrated
diagnosis in line with the WHO classification 2016. In
conclusion, cGBM does not represent a molecularly uniform
tumor entity, but rather comprises different brain tumor
entities with diverse prognosis and therapeutic options.
Distinction of these molecular tumor classes requires
molecular analysis. More than $30\%$ of tumors diagnosed as
cGBM belong to the recently described molecular entity of
anaplastic astrocytoma with piloid features.},
cin = {B300 / B360 / L101 / L401 / L601 / L201},
ddc = {610},
cid = {I:(DE-He78)B300-20160331 / I:(DE-He78)B360-20160331 /
I:(DE-He78)L101-20160331 / I:(DE-He78)L401-20160331 /
I:(DE-He78)L601-20160331 / I:(DE-He78)L201-20160331},
pnm = {312 - Functional and structural genomics (POF3-312)},
pid = {G:(DE-HGF)POF3-312},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:31661039},
pmc = {pmc:PMC6816155},
doi = {10.1186/s40478-019-0801-8},
url = {https://inrepo02.dkfz.de/record/147394},
}