000148818 001__ 148818 000148818 005__ 20240229123035.0 000148818 0247_ $$2doi$$a10.1111/nan.12590 000148818 0247_ $$2pmid$$apmid:31867747 000148818 0247_ $$2ISSN$$a0305-1846 000148818 0247_ $$2ISSN$$a1365-2990 000148818 0247_ $$2altmetric$$aaltmetric:73201637 000148818 037__ $$aDKFZ-2020-00010 000148818 041__ $$aeng 000148818 082__ $$a610 000148818 1001_ $$0P:(DE-He78)ce7d0cd1f5edc5c0e08c39b3fdd7b410$$aDeng, Maximilian Yuanzhe$$b0$$eFirst author$$udkfz 000148818 245__ $$aDiffuse Glioneuronal tumour with Oligodendroglioma-like features and Nuclear Clusters (DGONC) - a molecularly-defined glioneuronal CNS tumour class displaying recurrent monosomy 14. 000148818 260__ $$aOxford [u.a.]$$bWiley-Blackwell$$c2020 000148818 3367_ $$2DRIVER$$aarticle 000148818 3367_ $$2DataCite$$aOutput Types/Journal article 000148818 3367_ $$0PUB:(DE-HGF)16$$2PUB:(DE-HGF)$$aJournal Article$$bjournal$$mjournal$$s1601362992_26320 000148818 3367_ $$2BibTeX$$aARTICLE 000148818 3367_ $$2ORCID$$aJOURNAL_ARTICLE 000148818 3367_ $$00$$2EndNote$$aJournal Article 000148818 500__ $$a2020 Aug;46(5):422-430#EA:B360#LA:B300# 000148818 520__ $$aDNA methylation-based central nervous system (CNS) tumour classification has identified numerous molecularly-distinct tumour types, and clinically relevant subgroups among known CNS tumour entities that were previously thought to represent homogeneous diseases. Our study aimed at characterising a novel, molecularly-defined variant of glioneuronal CNS tumour.DNA methylation profiling was performed using the Infinium MethylationEPIC or 450k BeadChip arrays (Illumina) and analysed using the 'conumee' package in R computing environment. Additional gene panel sequencing was also performed. Tumour samples were collected at the German Cancer Research Centre (DKFZ) and provided by multi-national collaborators. Histological sections were also collected and independently reviewed.Genome-wide DNA methylation data from >25,000 CNS tumours were screened for clusters separated from established DNA methylation classes, revealing a novel group comprising 31 tumours, mainly found in paediatric patients. This DNA methylation-defined variant of low-grade CNS tumours with glioneuronal differentiation displays recurrent monosomy 14, nuclear clusters within a morphology that is otherwise reminiscent of oligodendroglioma and other established entities with clear-cell histology, and a lack of genetic alterations commonly observed in other (paediatric) glioneuronal entities.DNA methylation-based tumour classification is an objective method of assessing tumour origins, which may aid in diagnosis, especially for atypical cases. With increasing sample size, methylation analysis allows for the identification of rare, putative new tumour entities, which are currently not recognized by the WHO classification. Our study revealed the existence of a DNA methylation-defined class of low-grade glioneuronal tumours with recurrent monosomy 14, oligodendroglioma-like features and nuclear clusters. 000148818 536__ $$0G:(DE-HGF)POF3-312$$a312 - Functional and structural genomics (POF3-312)$$cPOF3-312$$fPOF III$$x0 000148818 588__ $$aDataset connected to CrossRef, PubMed, 000148818 7001_ $$0P:(DE-He78)45440b44791309bd4b7dbb4f73333f9b$$aSill, Martin$$b1$$udkfz 000148818 7001_ $$0P:(DE-He78)a46a5b2a871859c8e2d63d2f8c666807$$aSturm, Dominik$$b2$$udkfz 000148818 7001_ $$0P:(DE-He78)d20d08adc992abdb6ccffa1686f1ba17$$aStichel, Damian$$b3$$udkfz 000148818 7001_ $$0P:(DE-He78)046fd145f1008f83f6236580727bbc0f$$aWitt, Hendrik$$b4$$udkfz 000148818 7001_ $$0P:(DE-He78)3de637452ba900e2bdd359b8f41953bf$$aEcker, Jonas$$b5$$udkfz 000148818 7001_ $$0P:(DE-HGF)0$$aWittmann, Andreas$$b6 000148818 7001_ $$aSchittenhelm, Jens$$b7 000148818 7001_ $$aEbinger, Martin$$b8 000148818 7001_ $$aSchuhmann, Martin U$$b9 000148818 7001_ $$aFigarella-Branger, Dominique$$b10 000148818 7001_ $$aAronica, Eleonora$$b11 000148818 7001_ $$aStaszewski, Ori$$b12 000148818 7001_ $$aPreusser, Matthias$$b13 000148818 7001_ $$aHaberler, Christine$$b14 000148818 7001_ $$aLauten, Melchior$$b15 000148818 7001_ $$aSchüller, Ulrich$$b16 000148818 7001_ $$aHartmann, Christian$$b17 000148818 7001_ $$aSnuderl, Matija$$b18 000148818 7001_ $$aDunham, Christopher$$b19 000148818 7001_ $$aJabado, Nada$$b20 000148818 7001_ $$aWesseling, Pieter$$b21 000148818 7001_ $$aDeckert, Martina$$b22 000148818 7001_ $$aKeyvani, Kathy$$b23 000148818 7001_ $$aGottardo, Nick$$b24 000148818 7001_ $$aGiangaspero, Felice$$b25 000148818 7001_ $$avon Hoff, Katja$$b26 000148818 7001_ $$aEllison, David W$$b27 000148818 7001_ $$aPietsch, Torsten$$b28 000148818 7001_ $$aHerold Mende, Christel$$b29 000148818 7001_ $$0P:(DE-He78)0be2f86573954f87e97f8a4dbb05cb0f$$aMilde, Till$$b30$$udkfz 000148818 7001_ $$0P:(DE-He78)143af26de9d57bf624771616318aaf7c$$aWitt, 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