000167192 001__ 167192 000167192 005__ 20240229133533.0 000167192 0247_ $$2doi$$a10.1016/S2352-4642(20)30275-3 000167192 0247_ $$2pmid$$apmid:33484663 000167192 0247_ $$2altmetric$$aaltmetric:98629881 000167192 037__ $$aDKFZ-2021-00183 000167192 041__ $$aeng 000167192 082__ $$a610 000167192 1001_ $$aKratz, Christian P$$b0 000167192 245__ $$aPredisposition to cancer in children and adolescents. 000167192 260__ $$aKidlington, Oxford$$bElsevier$$c2021 000167192 3367_ $$2DRIVER$$aarticle 000167192 3367_ $$2DataCite$$aOutput Types/Journal article 000167192 3367_ $$0PUB:(DE-HGF)16$$2PUB:(DE-HGF)$$aJournal Article$$bjournal$$mjournal$$s1692790920_16395$$xReview Article 000167192 3367_ $$2BibTeX$$aARTICLE 000167192 3367_ $$2ORCID$$aJOURNAL_ARTICLE 000167192 3367_ $$00$$2EndNote$$aJournal Article 000167192 520__ $$aChildhood malignancies are rarely related to known environmental exposures, and it has become increasingly evident that inherited genetic factors play a substantial causal role. Large-scale sequencing studies have shown that approximately 10% of children with cancer have an underlying cancer predisposition syndrome. The number of recognised cancer predisposition syndromes and cancer predisposition genes are constantly growing. Imaging and laboratory technologies are improving, and knowledge of the range of tumours and risk of malignancy associated with cancer predisposition syndromes is increasing over time. Consequently, surveillance measures need to be constantly adjusted to address these new findings. Management recommendations for individuals with pathogenic germline variants in cancer predisposition genes need to be established through international collaborative studies, addressing issues such as genetic counselling, cancer prevention, cancer surveillance, cancer therapy, psychological support, and social-ethical issues. This Review represents the work by a group of experts from the European Society for Paediatric Oncology (SIOPE) and aims to summarise the current knowledge and define future research needs in this evolving field. 000167192 536__ $$0G:(DE-HGF)POF4-312$$a312 - Funktionelle und strukturelle Genomforschung (POF4-312)$$cPOF4-312$$fPOF IV$$x0 000167192 588__ $$aDataset connected to CrossRef, PubMed, 000167192 7001_ $$aJongmans, Marjolijn C$$b1 000167192 7001_ $$aCavé, Hélène$$b2 000167192 7001_ $$aWimmer, Katharina$$b3 000167192 7001_ $$aBehjati, Sam$$b4 000167192 7001_ $$aGuerrini-Rousseau, Lea$$b5 000167192 7001_ $$0P:(DE-He78)0be2f86573954f87e97f8a4dbb05cb0f$$aMilde, Till$$b6$$udkfz 000167192 7001_ $$0P:(DE-He78)a7c1bbac024fa232d9c6b78443328d9d$$aPajtler, Kristian W$$b7$$udkfz 000167192 7001_ $$aGolmard, Lisa$$b8 000167192 7001_ $$aGauthier-Villars, Marion$$b9 000167192 7001_ $$aJewell, Rosalyn$$b10 000167192 7001_ $$aDuncan, Catriona$$b11 000167192 7001_ $$aMaher, Eamonn R$$b12 000167192 7001_ $$aBrugieres, Laurence$$b13 000167192 7001_ $$aPritchard-Jones, Kathy$$b14 000167192 7001_ $$aBourdeaut, Franck$$b15 000167192 773__ $$0PERI:(DE-600)2900829-3$$a10.1016/S2352-4642(20)30275-3$$gVol. 5, no. 2, p. 142 - 154$$n2$$p142 - 154$$tThe lancet child & adolescent health$$v5$$x2352-4642$$y2021 000167192 909CO $$ooai:inrepo02.dkfz.de:167192$$pVDB 000167192 9101_ $$0I:(DE-588b)2036810-0$$6P:(DE-He78)0be2f86573954f87e97f8a4dbb05cb0f$$aDeutsches Krebsforschungszentrum$$b6$$kDKFZ 000167192 9101_ $$0I:(DE-588b)2036810-0$$6P:(DE-He78)a7c1bbac024fa232d9c6b78443328d9d$$aDeutsches Krebsforschungszentrum$$b7$$kDKFZ 000167192 9131_ $$0G:(DE-HGF)POF4-312$$1G:(DE-HGF)POF4-310$$2G:(DE-HGF)POF4-300$$3G:(DE-HGF)POF4$$4G:(DE-HGF)POF$$aDE-HGF$$bGesundheit$$lKrebsforschung$$vFunktionelle und strukturelle Genomforschung$$x0 000167192 9130_ $$0G:(DE-HGF)POF3-312$$1G:(DE-HGF)POF3-310$$2G:(DE-HGF)POF3-300$$3G:(DE-HGF)POF3$$4G:(DE-HGF)POF$$aDE-HGF$$bGesundheit$$lKrebsforschung$$vFunctional and structural genomics$$x0 000167192 9141_ $$y2021 000167192 915__ $$0StatID:(DE-HGF)0200$$2StatID$$aDBCoverage$$bSCOPUS$$d2020-09-03 000167192 915__ $$0StatID:(DE-HGF)0300$$2StatID$$aDBCoverage$$bMedline$$d2020-09-03 000167192 915__ $$0StatID:(DE-HGF)0199$$2StatID$$aDBCoverage$$bClarivate Analytics Master Journal List$$d2020-09-03 000167192 915__ $$0StatID:(DE-HGF)0160$$2StatID$$aDBCoverage$$bEssential Science Indicators$$d2020-09-03 000167192 915__ $$0StatID:(DE-HGF)1110$$2StatID$$aDBCoverage$$bCurrent Contents - Clinical Medicine$$d2020-09-03 000167192 915__ $$0StatID:(DE-HGF)0113$$2StatID$$aWoS$$bScience Citation Index Expanded$$d2020-09-03 000167192 915__ $$0StatID:(DE-HGF)0150$$2StatID$$aDBCoverage$$bWeb of Science Core Collection$$d2020-09-03 000167192 9201_ $$0I:(DE-He78)B310-20160331$$kB310$$lKKE Pädiatrische Onkologie$$x0 000167192 9201_ $$0I:(DE-He78)HD01-20160331$$kHD01$$lDKTK HD zentral$$x1 000167192 9201_ $$0I:(DE-He78)B062-20160331$$kB062$$lB062 Pädiatrische Neuroonkologie$$x2 000167192 980__ $$ajournal 000167192 980__ $$aVDB 000167192 980__ $$aI:(DE-He78)B310-20160331 000167192 980__ $$aI:(DE-He78)HD01-20160331 000167192 980__ $$aI:(DE-He78)B062-20160331 000167192 980__ $$aUNRESTRICTED