TY - JOUR AU - Glöss, Stefanie AU - Jurmeister, Philipp AU - Thieme, Anne AU - Schmid, Simone AU - Cai, Wei Y AU - Serrette, Rene N AU - Perner, Sven AU - Ribbat-Idel, Julika AU - Pagenstecher, Axel AU - Bläker, Hendrik AU - Keber, Ursula AU - Stadelmann, Christine AU - Zechel, Sabrina AU - Johann, Pascal D AU - Hasselblatt, Martin AU - Paulus, Werner AU - Thomas, Christian AU - Dohmen, Hildegard AU - Baumhoer, Daniel AU - Frank, Stephan AU - Agaimy, Abbas AU - Schüller, Ulrich AU - Vasudevaraja, Varshini AU - Snuderl, Matija AU - Liu, Cheng Z AU - Pfister, David G AU - Jungbluth, Achim A AU - Ghossein, Ronald A AU - Xu, Bin AU - Capper, David AU - Dogan, Snjezana TI - IDH2 R172 Mutations Across Poorly Differentiated Sinonasal Tract Malignancies: Forty Molecularly Homogenous and Histologically Variable Cases With Favorable Outcome. JO - The American journal of surgical pathology VL - 45 IS - 9 SN - 0147-5185 CY - [S.l.] PB - Ovid M1 - DKFZ-2021-01583 SP - 1190-1204 PY - 2021 N1 - 2021 Sep 1;45(9):1190-1204 AB - IDH2 R172 mutations occur in sinonasal undifferentiated carcinoma (SNUC), large-cell neuroendocrine carcinoma (LCNEC), sinonasal adenocarcinomas, and olfactory neuroblastoma (ONB). We performed a clinical, pathologic, and genetic/epigenetic analysis of a large IDH2-mutated sinonasal tumor cohort to explore their distinct features. A total 165 sinonasal/skull base tumors included 40 IDH2 mutants studied by light microscopy, immunohistochemistry, and genome-wide DNA methylation, and 125 IDH2 wild-type tumors used for comparison. Methylation profiles were analyzed by unsupervised hierarchical clustering, t-distributed stochastic neighbor embedding dimensionality reduction and assessed for copy number alterations (CNA). Thirty-nine histologically assessable cases included 25 (64.1 LB - PUB:(DE-HGF)16 C6 - pmid:34265800 DO - DOI:10.1097/PAS.0000000000001697 UR - https://inrepo02.dkfz.de/record/169840 ER -