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@ARTICLE{Hau:169962,
author = {P. Hau and D. Frappaz and E. Hovey and M. G. McCabe and K.
W. Pajtler$^*$ and B. Wiestler and C. Seidel and S. E. Combs
and L. Dirven and M. Klein and A. Anazodo and E. Hattingen
and S. Hofer and S. M. Pfister$^*$ and C. Zimmer and R.-D.
Kortmann and M.-P. Sunyach and R. Tanguy and R. Effeney and
A. von Deimling$^*$ and F. Sahm$^*$ and S. Rutkowski$^*$ and
A. S. Berghoff and E. Franceschi and E. Pineda and D. Beier
and E. Peeters and T. Gorlia and M. Vanlancker and J. E. C.
Bromberg and J. Gautier and D. S. Ziegler and M. Preusser
and W. Wick$^*$ and M. Weller},
title = {{D}evelopment of {R}andomized {T}rials in {A}dults with
{M}edulloblastoma-{T}he {E}xample of {EORTC}
1634-{BTG}/{NOA}-23.},
journal = {Cancers},
volume = {13},
number = {14},
issn = {2072-6694},
address = {Basel},
publisher = {MDPI},
reportid = {DKFZ-2021-01662},
pages = {3451},
year = {2021},
abstract = {Medulloblastoma is a rare brain malignancy. Patients after
puberty are rare and bear an intermediate prognosis.
Standard treatment consists of maximal resection plus
radio-chemotherapy. Treatment toxicity is high and produces
disabling long-term side effects. The sonic hedgehog (SHH)
subgroup is highly overrepresented in the post-pubertal and
adult population and can be targeted by smoothened (SMO)
inhibitors. No practice-changing prospective randomized data
have been generated in adults. The EORTC 1634-BTG/NOA-23
trial will randomize patients between standard-dose vs.
reduced-dosed craniospinal radiotherapy and SHH-subgroup
patients between the SMO inhibitor sonidegib (OdomzoTM, Sun
Pharmaceuticals Industries, Inc., New York, USA) in addition
to standard radio-chemotherapy vs. standard
radio-chemotherapy alone to improve outcomes in view of
decreased radiotherapy-related toxicity and increased
efficacy. We will further investigate tumor tissue, blood,
and cerebrospinal fluid as well as magnetic resonance
imaging and radiotherapy plans to generate information that
helps to further improve treatment outcomes. Given that
treatment side effects typically occur late, long-term
follow-up will monitor classic side effects of therapy, but
also health-related quality of life, cognition, social and
professional outcome, and reproduction and fertility. In
summary, we will generate unprecedented data that will be
translated into treatment changes in post-pubertal patients
with medulloblastoma and will help to design future clinical
trials.},
subtyp = {Review Article},
keywords = {adult (Other) / cerebrospinal fluid (Other) / chemotherapy
(Other) / clinical trial (Other) / magnetic resonance
imaging (Other) / medulloblastoma (Other) / radiotherapy
(Other) / randomized (Other) / subgrouping (Other) /
targeted therapy (Other)},
cin = {HD01 / B062 / B320},
ddc = {610},
cid = {I:(DE-He78)HD01-20160331 / I:(DE-He78)B062-20160331 /
I:(DE-He78)B320-20160331},
pnm = {312 - Funktionelle und strukturelle Genomforschung
(POF4-312)},
pid = {G:(DE-HGF)POF4-312},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:34298664},
doi = {10.3390/cancers13143451},
url = {https://inrepo02.dkfz.de/record/169962},
}