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@ARTICLE{Miao:179064,
author = {B. Miao$^*$ and D. Skopelitou$^*$ and A. Srivastava$^*$ and
S. Giangiobbe$^*$ and D. Dymerska and N. Paramasivam and A.
Kumar$^*$ and M. Kuświk and W. Kluźniak and K.
Paszkowska-Szczur and M. Schlesner$^*$ and J. Lubinski and
K. Hemminki$^*$ and A. Försti$^*$ and O. R. Bandapalli$^*$},
title = {{W}hole-{E}xome {S}equencing {I}dentifies a {N}ovel
{G}ermline {V}ariant in {PTK}7 {G}ene in {F}amilial
{C}olorectal {C}ancer.},
journal = {International journal of molecular sciences},
volume = {23},
number = {3},
issn = {1422-0067},
address = {Basel},
publisher = {Molecular Diversity Preservation International},
reportid = {DKFZ-2022-00442},
pages = {1295},
year = {2022},
note = {#EA:B062#LA:B062#},
abstract = {Colorectal cancer (CRC) is the third most frequently
diagnosed malignancy worldwide. Only $5\%$ of all CRC cases
are due to germline mutations in known predisposition genes,
and the remaining genetic burden still has to be discovered.
In this study, we performed whole-exome sequencing on six
members of a Polish family diagnosed with CRC and identified
a novel germline variant in the protein tyrosine kinase 7
(inactive) gene (PTK7, ENST00000230419, V354M). Targeted
screening of the variant in 1705 familial CRC cases and 1674
healthy elderly individuals identified the variant in an
additional familial CRC case. Introduction of this variant
in HT-29 cells resulted in increased cell proliferation,
migration, and invasion; it also caused down-regulation of
CREB, p21 and p53 mRNA and protein levels, and increased AKT
phosphorylation. These changes indicated inhibition of
apoptosis pathways and activation of AKT signaling. Our
study confirmed the oncogenic function of PTK7 and supported
its role in genetic predisposition of familial CRC.},
keywords = {Aged / Cell Adhesion Molecules: genetics / Cell Adhesion
Molecules: metabolism / Cell Movement: genetics / Cell
Proliferation: genetics / Colorectal Neoplasms: genetics /
Colorectal Neoplasms: pathology / Cyclic AMP Response
Element-Binding Protein: genetics / Cyclin-Dependent Kinase
Inhibitor p21: genetics / Family / Female / Genetic
Predisposition to Disease / Germ-Line Mutation: genetics /
Humans / Male / Middle Aged / Neoplasm Invasiveness:
genetics / Oncogenes / Pedigree / Proto-Oncogene Proteins
c-akt: genetics / Receptor Protein-Tyrosine Kinases:
genetics / Receptor Protein-Tyrosine Kinases: metabolism /
Tumor Suppressor Protein p53: genetics / Whole Exome
Sequencing: methods / AKT signaling pathway (Other) / PTK7
(Other) / colorectal cancer (Other) / familial cancer
variant prioritization pipeline (Other) / familial cancers
(Other) / germline variant (Other) / CDKN1A protein, human
(NLM Chemicals) / CREB1 protein, human (NLM Chemicals) /
Cell Adhesion Molecules (NLM Chemicals) / Cyclic AMP
Response Element-Binding Protein (NLM Chemicals) /
Cyclin-Dependent Kinase Inhibitor p21 (NLM Chemicals) /
Tumor Suppressor Protein p53 (NLM Chemicals) / PTK7 protein,
human (NLM Chemicals) / Receptor Protein-Tyrosine Kinases
(NLM Chemicals) / Proto-Oncogene Proteins c-akt (NLM
Chemicals)},
cin = {B062 / HD01 / C050 / W610},
ddc = {540},
cid = {I:(DE-He78)B062-20160331 / I:(DE-He78)HD01-20160331 /
I:(DE-He78)C050-20160331 / I:(DE-He78)W610-20160331},
pnm = {312 - Funktionelle und strukturelle Genomforschung
(POF4-312)},
pid = {G:(DE-HGF)POF4-312},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:35163215},
pmc = {pmc:PMC8836109},
doi = {10.3390/ijms23031295},
url = {https://inrepo02.dkfz.de/record/179064},
}