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@ARTICLE{Franceschi:181119,
author = {E. Franceschi and C. Giannini and J. Furtner and K.
Pajtler$^*$ and S. Asioli and R. Guzman and C. Seidel and L.
Gatto and P. Hau},
title = {{A}dult {M}edulloblastoma: {U}pdates on {C}urrent
{M}anagement and {F}uture {P}erspectives.},
journal = {Cancers},
volume = {14},
number = {15},
issn = {2072-6694},
address = {Basel},
publisher = {MDPI},
reportid = {DKFZ-2022-01788},
pages = {3708},
year = {2022},
abstract = {Medulloblastoma (MB) is a malignant embryonal tumor of the
posterior fossa belonging to the family of primitive
neuro-ectodermic tumors (PNET). MB generally occurs in
pediatric age, but in $14-30\%$ of cases, it affects the
adults, mostly below the age of 40, with an incidence of 0.6
per million per year, representing about $0.4-1\%$ of tumors
of the nervous system in adults. Unlike pediatric MB, robust
prospective trials are scarce for the post-puberal
population, due to the low incidence of MB in adolescent and
young adults. Thus, current MB treatments for older patients
are largely extrapolated from the pediatric experience, but
the transferability and applicability of these paradigms to
adults remain an open question. Adult MB is distinct from MB
in children from a molecular and clinical perspective. Here,
we review the management of adult MB, reporting the recent
published literature focusing on the effectiveness of
upfront chemotherapy, the development of targeted therapies,
and the potential role of a reduced dose of radiotherapy in
treating this disease.},
subtyp = {Review Article},
keywords = {SHH inhibitors (Other) / SHH pathway (Other) / chemotherapy
(Other) / medulloblastoma (Other) / neurosurgery (Other) /
radiotherapy (Other) / sonic hedgehog (SHH) (Other) /
sonidegib (Other) / targeted therapy (Other) / vismodegib
(Other)},
cin = {B062 / HD01},
ddc = {610},
cid = {I:(DE-He78)B062-20160331 / I:(DE-He78)HD01-20160331},
pnm = {312 - Funktionelle und strukturelle Genomforschung
(POF4-312)},
pid = {G:(DE-HGF)POF4-312},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:35954372},
doi = {10.3390/cancers14153708},
url = {https://inrepo02.dkfz.de/record/181119},
}