% IMPORTANT: The following is UTF-8 encoded. This means that in the presence
% of non-ASCII characters, it will not work with BibTeX 0.99 or older.
% Instead, you should use an up-to-date BibTeX implementation like “bibtex8” or
% “biber”.
@ARTICLE{Capper:186735,
author = {D. Capper$^*$ and G. Reifenberger$^*$ and P. J. French and
L. Schweizer$^*$ and M. Weller and M. Touat and S. P. Niclou
and P. Euskirchen and C. Haberler and M. E. Hegi and S.
Brandner and E. Le Rhun and R. Rudà and M. Sanson and G.
Tabatabai$^*$ and F. Sahm$^*$ and P. Y. Wen and P. Wesseling
and M. Preusser and M. J. van den Bent},
title = {{EANO} guideline on rational molecular testing of gliomas,
glioneuronal and neuronal tumors in adults for targeted
therapy selection.},
journal = {Neuro-Oncology},
volume = {25},
number = {5},
issn = {1522-8517},
address = {Oxford},
publisher = {Oxford Univ. Press},
reportid = {DKFZ-2023-00087},
pages = {813-826},
year = {2023},
note = {2023 May 4;25(5):813-826},
abstract = {The mainstay of treatment for adult patients with gliomas,
glioneuronal and neuronal tumors consists of combinations of
surgery, radiotherapy and chemotherapy. For many systemic
cancers, targeted treatments are a part of standard of care,
however the predictive significance of most of these targets
in CNS tumors remains less well studied. Despite that, there
is an increasing use of advanced molecular diagnostics that
identify potential targets, and tumor agnostic regulatory
approvals on targets also present in CNS tumors have been
granted. This raises the question when and for which targets
it is meaningful to test in adult patients with CNS tumors.
This evidence based guideline reviews the evidence available
for targeted treatment for alterations in the RAS/MAPK
pathway (BRAF, NF1), in growth factor receptors (EGFR, ALK,
FGFR, NTRK, PDGFRA, ROS1), in cell cycle signaling (CDK4/6,
MDM2/4, TSC1/2) and altered genomic stability (mismatch
repair, POLE, high TMB, HRD) in adult patients with gliomas,
glioneuronal and neuronal tumors. At present, targeted
treatment for BRAF p.V600E alterations is to be considered
part of standard of care for patients with recurrent
gliomas, pending regulatory approval. For approved tumor
agnostic treatments for NTRK fusions and high TMB, the
evidence for efficacy in adult patients with CNS tumors is
very limited, and treatment should preferably be given
within prospective clinical registries and trials. For
targeted treatment of CNS tumors with FGFR fusions or
mutations, clinical trials are ongoing to confirm modest
activity so far observed in basket trials. For all other
reviewed targets, evidence of benefit in CNS tumors is
currently lacking, and testing/treatment should be in the
context of available clinical trials.},
keywords = {Adults (Other) / EANO (Other) / Glioma (Other) / Guideline
(Other) / Targeted treatments (Other)},
cin = {BE01 / FM01 / TU01 / HD01 / ED01 / B300},
ddc = {610},
cid = {I:(DE-He78)BE01-20160331 / I:(DE-He78)FM01-20160331 /
I:(DE-He78)TU01-20160331 / I:(DE-He78)HD01-20160331 /
I:(DE-He78)ED01-20160331 / I:(DE-He78)B300-20160331},
pnm = {312 - Funktionelle und strukturelle Genomforschung
(POF4-312)},
pid = {G:(DE-HGF)POF4-312},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:36632791},
doi = {10.1093/neuonc/noad008},
url = {https://inrepo02.dkfz.de/record/186735},
}