% IMPORTANT: The following is UTF-8 encoded. This means that in the presence % of non-ASCII characters, it will not work with BibTeX 0.99 or older. % Instead, you should use an up-to-date BibTeX implementation like “bibtex8” or % “biber”. @ARTICLE{Stylianou:294406, author = {C. E. Stylianou and G. A. R. Wiggins and V. L. Lau and J. Dennis and A. N. Shelling and M. Wilson and P. Sykes and F. Amant and D. Annibali and W. De Wispelaere and D. F. Easton and P. A. Fasching and D. M. Glubb and E. L. Goode and D. Lambrechts and P. D. P. Pharoah and R. J. Scott and E. Tham and I. Tomlinson and M. K. Bolla and F. J. Couch and K. Czene and T. Dörk and A. M. Dunning and O. Fletcher and M. García-Closas and R. Hoppe and H. Jernström and R. Kaaks$^*$ and K. Michailidou and N. Obi and M. C. Southey and J. Stone and Q. Wang and A. B. Spurdle and T. A. O'Mara and J. Pearson and L. C. Walker}, collaboration = {A. Investigators}, othercontributors = {C. Clarke and D. Marsh and R. Scott and R. Baxter and D. Yip and J. Carpenter and A. Davis and N. Pathmanathan and P. Simpson and J. Dinny Graham and M. Sachchithananthan}, title = {{G}ermline copy number variants and endometrial cancer risk.}, journal = {Human genetics}, volume = {143}, issn = {0018-7348}, address = {Heidelberg}, publisher = {Springer}, reportid = {DKFZ-2024-02235}, pages = {1481–1498}, year = {2024}, note = {Volume 143, pages 1481–1498, (2024)}, abstract = {Known risk loci for endometrial cancer explain approximately one third of familial endometrial cancer. However, the association of germline copy number variants (CNVs) with endometrial cancer risk remains relatively unknown. We conducted a genome-wide analysis of rare CNVs overlapping gene regions in 4115 endometrial cancer cases and 17,818 controls to identify functionally relevant variants associated with disease. We identified a 1.22-fold greater number of CNVs in DNA samples from cases compared to DNA samples from controls (p = 4.4 × 10-63). Under three models of putative CNV impact (deletion, duplication, and loss of function), genome-wide association studies identified 141 candidate gene loci associated (p < 0.01) with endometrial cancer risk. Pathway analysis of the candidate loci revealed an enrichment of genes involved in the 16p11.2 proximal deletion syndrome, driven by a large recurrent deletion (chr16:29,595,483-30,159,693) identified in $0.15\%$ of endometrial cancer cases and $0.02\%$ of control participants. Together, these data provide evidence that rare copy number variants have a role in endometrial cancer susceptibility and that the proximal 16p11.2 BP4-BP5 region contains 25 candidate risk gene(s) that warrant further analysis to better understand their role in human disease.}, cin = {C020}, ddc = {610}, cid = {I:(DE-He78)C020-20160331}, pnm = {313 - Krebsrisikofaktoren und Prävention (POF4-313)}, pid = {G:(DE-HGF)POF4-313}, typ = {PUB:(DE-HGF)16}, pubmed = {pmid:39495297}, doi = {10.1007/s00439-024-02707-9}, url = {https://inrepo02.dkfz.de/record/294406}, }