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@PHDTHESIS{Gromann:294711,
author = {J. Großmann$^*$},
title = {{T}he regulation of polo-like kinase 4 in centrosome
duplication},
school = {Universität Heidelberg},
type = {Dissertation},
publisher = {Heidelberg University Library},
reportid = {DKFZ-2024-02444},
year = {2024},
note = {Dissertation, Universität Heidelberg, 2024},
abstract = {Centrosomes are important cell organelles that serve as
main microtubule-organizing centers and are involved in
diverse cellular processes, most importantly cell division
by facilitating formation of the bipolar spindle in mitosis.
Each centrosome consists of a pair of centrioles, which is
duplicated exactly once per cell cycle. The serine/threonine
protein kinase polo-like kinase 4, PLK4, is known as the
master regulator of centriole duplication. Overexpression of
PLK4 is sufficient to induce tumor formation in mice, by
causing centrosome amplification and chromosome
missegregation in mitosis as a source for genomic
instability. In order to prevent centriole overduplication,
PLK4 protein levels are tightly regulated by ubiquitylation
and proteasomal degradation. Protein ubiquitylation is a
post-translational modification, carried out by an enzymatic
cascade consisting of three enzymes: E1, E2 and E3. The
SKP1-CUL1-b-TrCP E3 ubiquitin ligase complex has been shown
to recognize the substrate PLK4 upon
trans-autophosphorylation of a degron motif and regulate its
protein levels by ubiquitylation and proteasomal
degradation. However, a b-TrCP binding mutant of PLK4 has
been found to be still ubiquitylated and partly degraded,
indicating that the exact regulation of PLK4 protein levels
has not been unraveled entirely yet. In the presented
thesis, I identified PLK4 as a novel substrate of the E3
ubiquitin ligase CUL4-DDB1-DCAF1, CRL4DCAF1, which
ubiquitylates and thereby targets PLK4 for degradation in G2
phase of the cell cycle to prevent premature centriole
duplication in mitosis. DCAF1 serves as a substrate binding
domain of the complex, which I showed to bind PLK4 in a
phosphorylation-independent manner. Overexpression of DCAF1
enhanced the ubiquitylation of PLK4, while knockdown of
DCAF1 increased PLK4 protein levels and caused the formation
of multipolar spindles in mitosis. I found that the
regulation of PLK4 by CRL4DCAF1 also affects the interaction
between PLK4 and its substrate STIL, as well as the process
of centriole disengagement at the onset of centriole
biogenesis. Taken together, I identified a new mechanism for
regulating PLK4 protein levels in centriole duplication that
is dependent on the CRL4DCAF1 ubiquitin ligase complex. My
results contribute to a better understanding of the complex
regulation and might open up new possibilities to target
deregulated or overexpressed PLK4 as a novel approach for
cancer therapy.},
keywords = {570 Life sciences (Other)},
cin = {D345},
cid = {I:(DE-He78)D345-20160331},
pnm = {314 - Immunologie und Krebs (POF4-314)},
pid = {G:(DE-HGF)POF4-314},
typ = {PUB:(DE-HGF)11},
doi = {10.11588/HEIDOK.00034989},
url = {https://inrepo02.dkfz.de/record/294711},
}