% IMPORTANT: The following is UTF-8 encoded. This means that in the presence
% of non-ASCII characters, it will not work with BibTeX 0.99 or older.
% Instead, you should use an up-to-date BibTeX implementation like “bibtex8” or
% “biber”.
@ARTICLE{Jessa:294723,
author = {S. Jessa and A. De Cola and B. Chandarana and M. McNicholas
and S. Hébert and A. Ptack and D. Faury and J. W. Tsai and
A. Korshunov$^*$ and T. N. Phoenix and B. Ellezam and D.
Jones$^*$ and M. D. Taylor and P. Bandopadhayay and M.
Pathania and N. Jabado and C. L. Kleinman},
title = {{FOXR}2 targets {LHX}6+/{DLX}+ neural lineages to drive
{CNS} neuroblastoma.},
journal = {Cancer research},
volume = {85},
number = {2},
issn = {0099-7013},
address = {Philadelphia, Pa.},
publisher = {AACR},
reportid = {DKFZ-2024-02456},
pages = {231-250},
year = {2025},
note = {2025 Jan 15;85(2):231-250},
abstract = {Central nervous system neuroblastoma with FOXR2 activation
(NB-FOXR2) is a high-grade tumor of the brain hemispheres
and a newly identified molecular entity. Tumors express dual
neuronal and glial markers, leading to frequent
misdiagnoses, and limited information exists on the role of
FOXR2 in their genesis. To identify their cellular origins,
we profiled the transcriptomes of NB-FOXR2 tumors at the
bulk and single-cell levels and integrated these profiles
with large single-cell references of the normal brain.
NB-FOXR2 tumors mapped to LHX6+/DLX+ lineages derived from
the medial ganglionic eminence, a progenitor domain in the
ventral telencephalon. In vivo prenatal Foxr2 targeting to
the ganglionic eminences in mice induced postnatal cortical
tumors recapitulating human NB-FOXR2 specific molecular
signatures. Profiling of FOXR2 binding on chromatin in
murine models revealed an association with ETS
transcriptional networks, as well as direct binding of FOXR2
at key transcription factors that coordinate initiation of
gliogenesis. These data indicate that NB-FOXR2 originate
from LHX6+/DLX+ interneuron lineages, a lineage-of-origin
distinct from that of other FOXR2-driven brain tumors,
highlight the susceptibility of ventral
telencephalon-derived interneurons to FOXR2-driven
oncogenesis, and suggest that FOXR2-induced activation of
glial programs may explain the mixed neuronal and
oligodendroglial features in these tumors. More broadly,
this work underscores systematic profiling of brain
development as an efficient approach to orient oncogenic
targeting for in vivo modeling, critical for the study of
rare tumors and development of therapeutics.},
cin = {B300 / HD01 / B360},
ddc = {610},
cid = {I:(DE-He78)B300-20160331 / I:(DE-He78)HD01-20160331 /
I:(DE-He78)B360-20160331},
pnm = {312 - Funktionelle und strukturelle Genomforschung
(POF4-312)},
pid = {G:(DE-HGF)POF4-312},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:39495206},
doi = {10.1158/0008-5472.CAN-24-2248},
url = {https://inrepo02.dkfz.de/record/294723},
}