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@ARTICLE{Mertlitz:300093,
author = {S. Mertlitz$^*$ and K. Riesner$^*$ and M. Kalupa$^*$ and N.
Uhlig$^*$ and S. Cordes$^*$ and L. Verlaat$^*$ and M.
Jamali$^*$ and N. Li$^*$ and H. M. E. R. Mohamed$^*$ and L.
Bullinger$^*$ and S. Moss and J. Greenwood and J. Jatzlau
and P. Knaus and P. Vallecillo-Garcia$^*$ and O. Penack$^*$},
title = {{L}eucine-rich α-2 glycoprotein 1 ({LRG}1) during
inflammatory complications after allogeneic stem cell
transplantation and {CAR}-{T} cell therapy.},
journal = {Journal for ImmunoTherapy of Cancer},
volume = {13},
number = {3},
issn = {2051-1426},
address = {London},
publisher = {BioMed Central},
reportid = {DKFZ-2025-00593},
pages = {e009372},
year = {2025},
abstract = {Previous data indicated that the leucine-rich α-2
glycoprotein 1 (LRG1) pathway contributes to vascular
dysfunction during cancer growth. Therapeutic targeting of
LRG1 normalized tumor vessel dysfunction and enhanced the
efficacy of anti-cancer adoptive T cell therapy. A major
clinical problem after allogeneic hematopoietic stem cell
transplantation (alloHSCT) and after chimeric antigen
receptor (CAR) T-cell therapy is the induction of
hyperinflammatory side effects, which are typically
associated with severe endothelial dysfunction.We
investigated LRG1 in preclinical models and in patient
samples.In prospective studies, we found elevated LRG1 serum
levels in patients with cytokine release syndrome and immune
effector cell-associated neurotoxicity syndrome after
CAR-T-cell therapy as well as in patients with acute
graft-versus-host disease (aGVHD) after alloHSCT.In
preclinical models of aGVHD, we found vasculature-associated
LRG1 upregulation as well as LRG1 pathway gene upregulation.
The genetic deletion of LRG1 in alloHSCT donors and in
alloHSCT recipients led to reduced clinical and histological
aGVHD. In line with this, LRG1 deletion led to clinically
and histologically reduced disease severity in experimental
inflammatory models of colitis (dextran sulfate sodium
colitis) and paw edema. LRG1 deletion reduced
inflammation-related vascular leakiness, endothelial cell
proliferation, and migration.The current data support the
hypothesis that LRG1 is an attractive therapeutic target
after alloHSCT and after CAR-T cell therapy for cancer
because of its role in dysfunctional tumor vessels as well
as in inflammatory complications.},
keywords = {Humans / Animals / Glycoproteins: metabolism / Mice /
Immunotherapy, Adoptive: methods / Immunotherapy, Adoptive:
adverse effects / Graft vs Host Disease: etiology /
Hematopoietic Stem Cell Transplantation: adverse effects /
Hematopoietic Stem Cell Transplantation: methods / Male /
Transplantation, Homologous / Female / Inflammation / Middle
Aged / Cytokine Release Syndrome: etiology / Receptors,
Chimeric Antigen: metabolism / Prospective Studies /
Cytokine release syndrome (Other) / Graft versus host
disease - GVHD (Other) / Immune related adverse event - irAE
(Other) / Immunotherapy (Other) / Stem cell (Other) / LRG1
protein, human (NLM Chemicals) / Glycoproteins (NLM
Chemicals) / LRG1 protein, mouse (NLM Chemicals) /
Receptors, Chimeric Antigen (NLM Chemicals)},
cin = {BE01},
ddc = {610},
cid = {I:(DE-He78)BE01-20160331},
pnm = {899 - ohne Topic (POF4-899)},
pid = {G:(DE-HGF)POF4-899},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:40118496},
doi = {10.1136/jitc-2024-009372},
url = {https://inrepo02.dkfz.de/record/300093},
}