% IMPORTANT: The following is UTF-8 encoded. This means that in the presence
% of non-ASCII characters, it will not work with BibTeX 0.99 or older.
% Instead, you should use an up-to-date BibTeX implementation like “bibtex8” or
% “biber”.
@ARTICLE{Gerhalter:300597,
author = {T. Gerhalter and B. Marty and L. V. Gast and F. Roemer and
P.-Y. Baudin and R. Trollmann and M. Uder and P. G. Carlier
and A. Nagel$^*$},
title = {{L}ongitudinal {F}ollow-{U}p of {P}atients {W}ith
{D}uchenne {M}uscular {D}ystrophy {U}sing {Q}uantitative
23{N}a and 1{H} {MRI}.},
journal = {Journal of cachexia, sarcopenia and muscle},
volume = {16},
number = {2},
issn = {2190-5991},
address = {Hoboken, NJ},
publisher = {Wiley},
reportid = {DKFZ-2025-00811},
pages = {e13812},
year = {2025},
note = {#LA:E020#},
abstract = {Quantitative muscle MRI commonly evaluates disease activity
and muscle wasting in Duchenne muscular dystrophy (DMD).
Disturbances in ion homeostasis contribute to DMD
pathophysiology, but their relationships with disease
progression is unclear. 23Na MRI may provide insights into
the disease course and treatment response. This longitudinal
study assessed whether sodium levels are elevated in DMD
patients regardless of fat fraction (FF) and whether
baseline sodium levels influence FF changes over time.
Additionally, we quantified the effect of slice selection on
measured sodium values.Thirteen DMD boys (age 7.8 ± 2.4
years) underwent MRI of lower leg muscles at 3T at three
visits, spaced 6 months apart. We assessed FF for disease
progression and water T2, pH, apparent tissue sodium
concentration (aTSC), and intracellular-weighted 23Na signal
(ICwS) for disease activity. Fourteen healthy boys (age 9.5
± 1.7 years) underwent the same MRI protocol once. Linear
regression and mixed-effect modelling were used to examine
sodium level increases and their impact on FF changes.In
DMD, muscles with FF < $10\%$ exhibited significantly
elevated aTSC (24.8 ± 4.6 mM vs. 14.5 ± 2.1 mM in
controls, p < 0.001) and higher ICwS (23.6 ± 2.5 a.u. vs.
14.1 ± 2.1 a.u., p < 0.001). At Visit 1, FF values showed a
significant negative association with aTSC (β = -17.30, p =
0.016) and ICwS (β = -21.02, p < 0.001). The first
mixed-effect model, which assessed aTSC alone, showed no
significant effect on FF progression but indicated a weak
trend (p = 0.098). The second, more comprehensive
model-incorporating also ICwS and water T2-revealed that FF
changes were positively associated with aTSC (p = 0.0023)
and negatively associated with ICwS and wT2 (p < 0.001 and p
= 0.025, respectively), with ICwS showing a significant
interaction with time (p = 0.0033). Varying slice
positioning and slice number demonstrated minimal impact on
aTSC and ICwS, with low CV $(2\%-4\%)$ in the mid-belly
region.The study demonstrates significant MRI-based changes
related to dystrophic alterations in DMD. We identified
early alterations in sodium homeostasis, independent of FF.
Our findings suggest that the relationship between sodium
levels and FF progression is complex and may not be fully
explained by total sodium measurements alone. Given the
small sample size, further validation in larger cohorts is
needed. Combined 1H and 23Na-MRI may offer deeper insights
into how metabolic and ionic changes interact with FF
progression and overall disease activity.},
keywords = {Humans / Muscular Dystrophy, Duchenne: diagnostic imaging /
Male / Child / Magnetic Resonance Imaging: methods /
Longitudinal Studies / Follow-Up Studies / Muscle, Skeletal:
diagnostic imaging / Disease Progression / Adolescent /
Sodium: metabolism / Duchenne muscular dystrophy (Other) /
fat fraction (Other) / muscle imaging (Other) / quantitative
MRI (Other) / skeletal muscle (Other) / sodium (Other) /
Sodium (NLM Chemicals)},
cin = {E020},
ddc = {610},
cid = {I:(DE-He78)E020-20160331},
pnm = {315 - Bildgebung und Radioonkologie (POF4-315)},
pid = {G:(DE-HGF)POF4-315},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:40254293},
doi = {10.1002/jcsm.13812},
url = {https://inrepo02.dkfz.de/record/300597},
}