% IMPORTANT: The following is UTF-8 encoded. This means that in the presence
% of non-ASCII characters, it will not work with BibTeX 0.99 or older.
% Instead, you should use an up-to-date BibTeX implementation like “bibtex8” or
% “biber”.
@ARTICLE{ConjardDuplany:300710,
author = {A. Conjard-Duplany and A. Osseni and A. Lamboux and S.
Mouradian and F. Picard and V. Moncollin and C. Angleraux
and T. Dorel-Dubois and H. Puccio and P. Leblanc and B.
Galy$^*$ and V. Balter and L. Schaeffer and Y.-G. Gangloff},
title = {{M}uscle m{TOR} controls iron homeostasis and
ferritinophagy via {NRF}2, {HIF}s and {AKT}/{PKB} signaling
pathways.},
journal = {Cellular and molecular life sciences},
volume = {82},
number = {1},
issn = {1420-682X},
address = {Cham (ZG)},
publisher = {Springer International Publishing AG},
reportid = {DKFZ-2025-00890},
pages = {178},
year = {2025},
abstract = {Balanced mTOR activity and iron levels are crucial for
muscle integrity, with evidence suggesting mTOR regulates
cellular iron homeostasis. In this study, we investigated
iron metabolism in muscle-specific mTOR knockout mice
(mTORmKO) and its relation to their myopathy. The mTORmKO
mice exhibited distinct iron content patterns across muscle
types and ages. Slow-twitch soleus muscles initially showed
reduced iron levels in young mice, which increased with the
dystrophy progression but remained within control ranges. In
contrast, the less affected fast-twitch muscles maintained
near-normal iron levels from a young age. Interestingly,
both mTORmKO muscle types exhibited iron metabolism markers
indicative of iron excess, including decreased transferrin
receptor 1 (TFR1) and increased levels of ferritin (FTL) and
ferroportin (FPN) proteins. Paradoxically, these changes
were accompanied by downregulated Ftl and Fpn mRNA levels,
indicating post-transcriptional regulation. This discordant
regulation resulted from disruption of key iron metabolism
pathways, including NRF2/NFE2L2, HIFs, and AKT/PKB
signaling. Mechanistically, mTOR deficiency impaired
transcriptional regulation of iron-related genes mediated by
NRF2 and HIFs. Furthermore, it triggered ferritin
accumulation through two NRF2 mechanisms: (1) derepression
of ferritin translation via suppression of the FBXL5-IRP
axis, and (2) autophagosomal sequestration driven by
NCOA4-dependent ferritin targeting to autophagosomes,
coupled with age-related impairments of autophagy linked to
chronic AKT/PKB activation. Three-week spermidine
supplementation in older mTORmKO mice was associated with
normalized AKT/PKB-FOXO signaling, increased endolysosomal
FTL and reduced total FTL levels in the dystrophic soleus
muscle. These findings underscore mTOR's crucial role in
skeletal muscle iron metabolism and suggest spermidine as a
potential strategy to address impaired ferritinophagy due to
autophagy blockade in dystrophic muscle.},
keywords = {Animals / TOR Serine-Threonine Kinases: metabolism / TOR
Serine-Threonine Kinases: genetics / Iron: metabolism /
Ferritins: metabolism / Ferritins: genetics / NF-E2-Related
Factor 2: metabolism / Homeostasis / Signal Transduction /
Proto-Oncogene Proteins c-akt: metabolism / Mice, Knockout /
Muscle, Skeletal: metabolism / Mice / Autophagy /
Ferroportin / Cation Transport Proteins: metabolism / Cation
Transport Proteins: genetics / Receptors, Transferrin:
metabolism / Basic Helix-Loop-Helix Transcription Factors:
metabolism / Mice, Inbred C57BL / Nuclear Receptor
Coactivators: metabolism / Male / Autophagy (Other) /
Dystrophy (Other) / Glycogen (Other) / Iron-sulfur cluster
(Other) / Myoglobin (Other) / Oxidative stress (Other) / TOR
Serine-Threonine Kinases (NLM Chemicals) / Iron (NLM
Chemicals) / Ferritins (NLM Chemicals) / NF-E2-Related
Factor 2 (NLM Chemicals) / Proto-Oncogene Proteins c-akt
(NLM Chemicals) / mTOR protein, mouse (NLM Chemicals) /
Ferroportin (NLM Chemicals) / Nfe2l2 protein, mouse (NLM
Chemicals) / Cation Transport Proteins (NLM Chemicals) /
Receptors, Transferrin (NLM Chemicals) / Basic
Helix-Loop-Helix Transcription Factors (NLM Chemicals) /
Nuclear Receptor Coactivators (NLM Chemicals)},
cin = {D430},
ddc = {610},
cid = {I:(DE-He78)D430-20160331},
pnm = {314 - Immunologie und Krebs (POF4-314)},
pid = {G:(DE-HGF)POF4-314},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:40293459},
doi = {10.1007/s00018-025-05695-9},
url = {https://inrepo02.dkfz.de/record/300710},
}