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@ARTICLE{Winkler:303488,
author = {M. Winkler and T. Staniczek and M. Suhayda and S. W.
Kürschner-Zacharias and J. Hoffmann and J. Cordero and L.
Kraske and H. Maude and D. Nagy and R. Manco and C. Sticht
and M. Neßling$^*$ and K. Richter$^*$ and G. Dobreva and A.
M. Randi and I. Cebola and K. Schledzewski and P.-S.
Reiners-Koch and S. Goerdt and C. D. Schmid},
title = {{E}ndothelial c-{M}af prevents {MASLD}-like liver fibrosis
by regulating chromatin accessibility to suppress pathogenic
microvascular cell subsets.},
journal = {JHEP reports},
volume = {7},
number = {9},
issn = {2589-5559},
address = {Amsterdam},
publisher = {Elsevier},
reportid = {DKFZ-2025-01679},
pages = {101475},
year = {2025},
abstract = {Liver sinusoidal endothelial cells (LSECs) are highly
specialized components of the hepatic vascular niche,
regulating liver function and disease pathogenesis through
angiocrine signaling. Recently, we identified GATA4 as a key
transcription factor controlling LSEC development and
protecting against liver fibrosis. As the transcription
factor c-Maf was strongly downregulated in Gata4-deficient
LSECs, we hypothesized that c-Maf might be an important
downstream effector of GATA4 in LSEC differentiation and
liver fibrogenesis.Clec4g-iCre/Maf fl/fl (Maf LSEC-KO ) mice
with LSEC-specific Maf deficiency were generated and liver
tissue was analyzed histologically. LSECs were isolated for
bulk RNA-seq, ATAC-seq, and single-cell (sc) RNA-seq
analysis. Maf LSEC-KO livers were analyzed after MASH diet
feeding. The expression of MAF and its targets was analyzed
in published human scRNA-seq data.Endothelial Maf deficiency
resulted in perisinusoidal liver fibrosis (Sirius red
$0.46\%$ vs. $2.92\%;$ p <0.05) without affecting metabolic
liver zonation, accompanied by a switch from sinusoidal to
continuous endothelial cell identity, which was aggravated
upon MASH diet feeding (p <0.01). Furthermore, endothelial
Maf deficiency caused LSEC proliferation (p <0.05) and
expression of profibrotic angiocrine factors including
Pdgfb, Igfbp5, Flrt2, and Cxcl12, among which FLRT2 (p
<0.01) and CXCL12 (p <0.001) activated hepatic stellate
cells in vitro. scRNA-seq revealed replacement of zonated
LSEC subpopulations with capillarized, proliferative,
sprouting and secretory endothelial cell subsets that
promote liver fibrogenesis and angiogenesis. This
fundamental dysregulation of LSEC gene expression and
differentiation was caused by changes in chromatin
accessibility and transcription factor activity following
loss of Maf. Notably, endothelial MAF expression was also
significantly reduced in human cirrhotic livers (p
<0.0001).Hepatic endothelial c-Maf protects against
metabolic dysfunction-associated steatohepatitis-like liver
fibrosis and regulates endothelial differentiation and
zonation by controlling chromatin opening.This work builds
on the known importance of liver sinusoidal endothelial
cells in liver function and disease. Here, transcription
factor c-Maf is identified as a master regulator in
maintaining normal differentiation and zonation of liver
sinusoidal endothelial cells, thereby protecting against the
development of liver fibrosis/cirrhosis. The findings are
significant for researchers and clinicians focusing on liver
disease, as they suggest potential new targets for
therapeutic intervention. These findings could instruct the
development of novel preventive treatment options and
antifibrotic therapy regimens as well as liver repair
strategies, benefiting patients, clinicians and policy
makers in the management of liver disease.},
keywords = {ATAC-Seq analysis (Other) / Capillarization (Other) /
Cirrhosis (Other) / Liver sinusoidal endothelial cells
(LSEC) (Other) / Single-cell RNA-Seq analysis (Other)},
cin = {W230},
ddc = {610},
cid = {I:(DE-He78)W230-20160331},
pnm = {319H - Addenda (POF4-319H)},
pid = {G:(DE-HGF)POF4-319H},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:40810103},
pmc = {pmc:PMC12341620},
doi = {10.1016/j.jhepr.2025.101475},
url = {https://inrepo02.dkfz.de/record/303488},
}