% IMPORTANT: The following is UTF-8 encoded. This means that in the presence % of non-ASCII characters, it will not work with BibTeX 0.99 or older. % Instead, you should use an up-to-date BibTeX implementation like “bibtex8” or % “biber”. @ARTICLE{SparberSauer:284983, author = {M. Sparber-Sauer and M. Dietzschold and A. Schönstein and A. Heinz and C. Vokuhl and K. Pajtler$^*$ and S. Harrabi$^*$ and Y.-L. Lin and T. v. Kalle and R. Hagen and R. Ladenstein and B. Kazanowska and G. Ljungman and T. Klingebiel and M. Ebinger and E. Koscielniak and M. Münter and B. Timmermann$^*$}, collaboration = {C. S. Group}, title = {{R}adiotherapy and long-term sequelae in pediatric patients with parameningeal rhabdomyosarcoma: {R}esults of two {C}ooperative {W}eichteilsarkom {S}tudiengruppe ({CWS}) trials and one registry.}, journal = {Pediatric blood $\&$ cancer}, volume = {71}, number = {1}, issn = {1545-5009}, address = {New York, NY}, publisher = {Wiley}, reportid = {DKFZ-2023-02167}, pages = {e30742}, year = {2024}, note = {2024 Jan;71(1):e30742}, abstract = {Parameningeal location of rhabdomyosarcoma (PM RMS) is known to be an unfavorable prognostic factor. Scarce data are available on radiotherapy (RT) concepts with regard to outcome.Treatment and outcome of 395 children with PM RMS registered within two Cooperative Weichteilsarkom Studiengruppe (CWS) trials and one registry (1995-2021) were evaluated.Patients were IRS group II (n = 15) and III (n = 380) and received systemic treatment according to the enrolled protocols: I2VA (n = 172), VAIA/CEVAIE (n = 223). Delayed resection was performed in 88/395 $(22\%)$ patients, and RT was additionally given in 79/88 $(90\%)$ resected patients. RT was the predominant local treatment in 355/395 $(90\%)$ patients: hyperfractionated accelerated photon (HART; n = 77), conventionally fractionated photon (n = 91) or proton beam (n = 126), brachytherapy (n = 4), heavy ions (n = 1), not available (n = 56). In the subgroup of RT as only local treatment (n = 278), no intracranial tumor extension and complete remission at end of treatment were significant positive prognostic factors. No significant difference on tumor outcome was seen between different radiotherapy concepts. Long-term toxicity with mostly endocrinological and visual deficiencies was reported in 161/279 $(58\%)$ surviving patients with a lower trend after proton beam RT $(48\%)$ when compared to HART or conventionally fractionated photon RT $(71\%$ and $72\%,$ respectively). Ten-year event-free and overall survival in the overall group were $62\%$ (±5, $95\%$ confidence interval [CI]) and $67\%$ (±5, $95\%$ CI); in the RT-only group $67\%$ (±6, $95\%$ CI) and $71\%$ (±6, $95\%$ CI), respectively.CWS data confirm the recent RT concept in PM RMS. Long-term sequelae as endocrinological and visual deficiencies need to be addressed.}, keywords = {CWS Group (Other) / children and adolescents (Other) / parameningeal rhabdomyosarcoma (Other) / proton beam irradiation (Other)}, cin = {B062 / HD01 / E050 / ED01}, ddc = {610}, cid = {I:(DE-He78)B062-20160331 / I:(DE-He78)HD01-20160331 / I:(DE-He78)E050-20160331 / I:(DE-He78)ED01-20160331}, pnm = {315 - Bildgebung und Radioonkologie (POF4-315)}, pid = {G:(DE-HGF)POF4-315}, typ = {PUB:(DE-HGF)16}, pubmed = {pmid:37880926}, doi = {10.1002/pbc.30742}, url = {https://inrepo02.dkfz.de/record/284983}, }