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@ARTICLE{Pepin:301272,
author = {M. E. Pepin and P. J. M. Konrad and S. Nazir and F. Bazgir
and C. Maack and A. Nickel and J. Gorman and M. Hohl and F.
Schreiter and M. Dewenter and A. de Britto Chaves Filho$^*$
and A. Schulze$^*$ and A. Karlstaedt and N. Frey and C.
Seidman and J. Seidman and J. Backs},
title = {{M}itochondrial {NNT} {P}romotes {D}iastolic {D}ysfunction
in {C}ardiometabolic {HF}p{EF}.},
journal = {Circulation research},
volume = {136},
number = {12},
issn = {0009-7330},
address = {New York, NY},
publisher = {Assoc.},
reportid = {DKFZ-2025-00957},
pages = {1564-1578},
year = {2025},
note = {2025 Jun 6;136(12):1564-1578},
abstract = {Clinical management of heart failure with preserved
ejection fraction (HFpEF) is hindered by a lack of
disease-modifying therapies capable of altering its distinct
pathophysiology. Despite the widespread implementation of a
2-hit model of cardiometabolic HFpEF to inform precision
therapy, which utilizes ad libitum high-fat diet and $0.5\%$
N(ω)-nitro-L-arginine methyl ester, we observe that
C57BL6/J mice exhibit less cardiac diastolic dysfunction in
response to high-fat diet and $0.5\%$ N(ω)-nitro-L-arginine
methyl ester.Genetic strain-specific single-nucleus
transcriptomic analysis identified disease-relevant genes
that enrich oxidative metabolic pathways within
cardiomyocytes. Because C57BL/6J mice are known to harbor a
loss-of-function mutation affecting the inner mitochondrial
membrane protein Nnt (nicotinamide nucleotide
transhydrogenase), we used an isogenic model of Nnt
loss-of-function to determine whether intact NNT is
necessary for the pathological cardiac manifestations of
high-fat diet and $0.5\%$ N(ω)-nitro-L-arginine methyl
ester. Twelve-week-old mice cross-bred to isolate wild-type
(Nnt+/+) or loss-of-function (Nnt-/-) Nnt in the C57BL/6N
background were challenged with high-fat diet and $0.5\%$
N(ω)-nitro-L-arginine methyl ester for 9 weeks
(n=6-10).Nnt+/+ mice exhibited impaired ventricular
diastolic relaxation and pathological remodeling, as
assessed via E/e' (42.8 versus 21.5, P=1.2×10-10), E/A (2.3
versus 1.4, P=4.1×10-2), diastolic stiffness (0.09 versus
0.04 mm Hg/μL, P=5.1×10-3), and myocardial fibrosis
(P=2.3×10-2). Liquid chromatography and mass spectroscopy
exposed a $40.0\%$ reduction in NAD+ (P=8.4×10-3) and a
$38.8\%$ reduction in glutathione:GSSG (P=2.6×10-2) among
Nnt+/+ mice after high-fat diet and $0.5\%$
N(ω)-nitro-L-arginine methyl ester feeding. Using
single-nucleus ligand-receptor analysis, we implicate Fgf1
(fibroblast growth factor 1) as a putative NNT-dependent
mediator of cardiomyocyte-to-fibroblast signaling of
myocardial fibrosis.Together, these findings underscore the
pivotal role of mitochondrial dysfunction in HFpEF
pathogenesis, implicating both NNT and Fgf1 as novel
therapeutic targets.},
keywords = {NG-nitroarginine methyl ester (Other) / fibrosis (Other) /
genetic therapy (Other) / heart failure (Other) / oxidative
stress (Other)},
cin = {A410},
ddc = {610},
cid = {I:(DE-He78)A410-20160331},
pnm = {311 - Zellbiologie und Tumorbiologie (POF4-311)},
pid = {G:(DE-HGF)POF4-311},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:40340422},
doi = {10.1161/CIRCRESAHA.125.326154},
url = {https://inrepo02.dkfz.de/record/301272},
}